Cardiomyopathies

Myocardial tuberculosis presenting as restrictive cardiomyopathy

Biopsy / Echocardiography / Tuberculosis / Humans / Male / Differential Diagnosis / Angiography / Adult / Myocardium / Public health systems and services research / Cardiomyopathies / Differential Diagnosis / Angiography / Adult / Myocardium / Public health systems and services research / Cardiomyopathies

Características clínicas, eletrocardiográficas e ecocardiográficas na amiloidose cardíaca significativa detectada apenas à necrópsia: comparação com casos diagnosticados em vida

Biopsy / Electrocardiography / Echocardiography / Heart Failure / Humans / Female / Male / Left Ventricular Dysfunction / Aged / Middle Aged / Autopsy / Myocardium / Cardiomyopathies / Heart Ventricles / Amyloidosis / Female / Male / Left Ventricular Dysfunction / Aged / Middle Aged / Autopsy / Myocardium / Cardiomyopathies / Heart Ventricles / Amyloidosis

Familial globotriaosylceramide-associated cardiomyopathy mimicking Fabry disease

Immunohistochemistry / Risk assessment / Heart Failure / Humans / Female / Male / Heart / Differential Diagnosis / Pedigree / Fabry Disease / Middle Aged / Adult / Survival Rate / Prognosis / Disease Progression / Risk Assessment / Cardiomyopathies / Male / Heart / Differential Diagnosis / Pedigree / Fabry Disease / Middle Aged / Adult / Survival Rate / Prognosis / Disease Progression / Risk Assessment / Cardiomyopathies

Fabry’s Disease Cardiomyopathy

Adolescent / Echocardiography / Humans / Female / Male / Magnetic Resonance / Differential Diagnosis / Fabry Disease / Aged / Middle Aged / Adult / Myocardium / Public health systems and services research / Cardiomyopathies / Sensitivity and Specificity / Hypertrophic Cardiomyopathy / Glycosphingolipids / The American / Magnetic Resonance / Differential Diagnosis / Fabry Disease / Aged / Middle Aged / Adult / Myocardium / Public health systems and services research / Cardiomyopathies / Sensitivity and Specificity / Hypertrophic Cardiomyopathy / Glycosphingolipids / The American

Cirrhotic Cardiomyopathy

Hepatology / Electrocardiography / Humans / Portal hypertension / Liver Cirrhosis / Animals / Calcium Signaling / Liver Transplantation / Fibrosis / Clinical Sciences / Nitric Oxide Synthase / Myocardium / Public health systems and services research / Baroreflex / Nervous System / Cardiomyopathies / Syndrome / Cardiac failure / The American / Animals / Calcium Signaling / Liver Transplantation / Fibrosis / Clinical Sciences / Nitric Oxide Synthase / Myocardium / Public health systems and services research / Baroreflex / Nervous System / Cardiomyopathies / Syndrome / Cardiac failure / The American

Reduced MMP-2 activity contributes to cardiac fibrosis in experimental diabetic cardiomyopathy

Extracellular Matrix / BASIC / Real-time RT-PCR / Diabetes mellitus / Collagen / Animals / Male / Digital Image Analysis / Fibrosis / mRna expression levels / Rats / Myocardium / Time Dependent / Diabetes complications / Western blot / Protein Expression / Transforming Growth Factor Beta / Ischemic Heart Disease / Basic Cardiology / Cardiomyopathies / Streptozotocin / Digital Image / Diabetic Rat / Left Ventricle / Matrix Metalloproteinase / Animals / Male / Digital Image Analysis / Fibrosis / mRna expression levels / Rats / Myocardium / Time Dependent / Diabetes complications / Western blot / Protein Expression / Transforming Growth Factor Beta / Ischemic Heart Disease / Basic Cardiology / Cardiomyopathies / Streptozotocin / Digital Image / Diabetic Rat / Left Ventricle / Matrix Metalloproteinase

Cirrhotic cardiomyopathy

Hepatology / Electrocardiography / Humans / Portal hypertension / Liver Cirrhosis / Animals / Calcium Signaling / Liver Transplantation / Fibrosis / Clinical Sciences / Nitric Oxide Synthase / Myocardium / Public health systems and services research / Baroreflex / Nervous System / Cardiomyopathies / Syndrome / Cardiac failure / The American / Animals / Calcium Signaling / Liver Transplantation / Fibrosis / Clinical Sciences / Nitric Oxide Synthase / Myocardium / Public health systems and services research / Baroreflex / Nervous System / Cardiomyopathies / Syndrome / Cardiac failure / The American

Cirrhotic Cardiomyopathy

Hepatology / Electrocardiography / Humans / Portal hypertension / Liver Cirrhosis / Animals / Calcium Signaling / Liver Transplantation / Fibrosis / Clinical Sciences / Nitric Oxide Synthase / Myocardium / Public health systems and services research / Baroreflex / Nervous System / Cardiomyopathies / Syndrome / Cardiac failure / The American / Animals / Calcium Signaling / Liver Transplantation / Fibrosis / Clinical Sciences / Nitric Oxide Synthase / Myocardium / Public health systems and services research / Baroreflex / Nervous System / Cardiomyopathies / Syndrome / Cardiac failure / The American

Diabetic cardiomyopathy: a controversial entity

Echocardiography / Humans / Cardiomyopathies / Type 2 Diabetes Mellitus

Echocardiographic Features of Genetic Diseases: Part 6. Complex Cardiovascular Defects

Genetics / Adolescent / Williams Syndrome / Down Syndrome / Echocardiography / Spleen / Congenital Heart Defects / Humans / Child / Female / Inborn errors of metabolism / Connective tissue / Marfan syndrome / Differential Diagnosis / Pheochromocytoma / Hemochromatosis / Fabry Disease / Aged / L-carnitine / Adult / Tuberous sclerosis / Genetic Disorder / Neoplasms / Ehlers-Danlos Syndrome / Reproducibility of Results / Noonan syndrome / Cardiomyopathies / Pericardium / Hypertrophic Cardiomyopathy / Aorta / Turner Syndrome / Gaucher Disease / Friedreich Ataxia / Myxoma / Heart Diseases / Spleen / Congenital Heart Defects / Humans / Child / Female / Inborn errors of metabolism / Connective tissue / Marfan syndrome / Differential Diagnosis / Pheochromocytoma / Hemochromatosis / Fabry Disease / Aged / L-carnitine / Adult / Tuberous sclerosis / Genetic Disorder / Neoplasms / Ehlers-Danlos Syndrome / Reproducibility of Results / Noonan syndrome / Cardiomyopathies / Pericardium / Hypertrophic Cardiomyopathy / Aorta / Turner Syndrome / Gaucher Disease / Friedreich Ataxia / Myxoma / Heart Diseases

Echocardiographic features of genetic diseases: Part 1. Cardiomyopathy

Genetics / Adolescent / Williams Syndrome / Down Syndrome / Echocardiography / Spleen / Congenital Heart Defects / Humans / Child / Female / Inborn errors of metabolism / Connective tissue / Marfan syndrome / Differential Diagnosis / Pheochromocytoma / Hemochromatosis / Fabry Disease / Aged / L-carnitine / Adult / Tuberous sclerosis / Genetic Disorder / Neoplasms / Ehlers-Danlos Syndrome / Reproducibility of Results / Noonan syndrome / Cardiomyopathies / Pericardium / Hypertrophic Cardiomyopathy / Aorta / Turner Syndrome / Gaucher Disease / Friedreich Ataxia / Myxoma / Heart Diseases / Spleen / Congenital Heart Defects / Humans / Child / Female / Inborn errors of metabolism / Connective tissue / Marfan syndrome / Differential Diagnosis / Pheochromocytoma / Hemochromatosis / Fabry Disease / Aged / L-carnitine / Adult / Tuberous sclerosis / Genetic Disorder / Neoplasms / Ehlers-Danlos Syndrome / Reproducibility of Results / Noonan syndrome / Cardiomyopathies / Pericardium / Hypertrophic Cardiomyopathy / Aorta / Turner Syndrome / Gaucher Disease / Friedreich Ataxia / Myxoma / Heart Diseases

Echocardiographic Features of Genetic Diseases: Part 4. Connective Tissue

Genetics / Adolescent / Williams Syndrome / Down Syndrome / Echocardiography / Spleen / Congenital Heart Defects / Humans / Child / Female / Inborn errors of metabolism / Connective tissue / Marfan syndrome / Differential Diagnosis / Pheochromocytoma / Hemochromatosis / Fabry Disease / Aged / L-carnitine / Adult / Tuberous sclerosis / Genetic Disorder / Neoplasms / Ehlers-Danlos Syndrome / Reproducibility of Results / Noonan syndrome / Cardiomyopathies / Pericardium / Hypertrophic Cardiomyopathy / Aorta / Turner Syndrome / Gaucher Disease / Friedreich Ataxia / Myxoma / Heart Diseases / Spleen / Congenital Heart Defects / Humans / Child / Female / Inborn errors of metabolism / Connective tissue / Marfan syndrome / Differential Diagnosis / Pheochromocytoma / Hemochromatosis / Fabry Disease / Aged / L-carnitine / Adult / Tuberous sclerosis / Genetic Disorder / Neoplasms / Ehlers-Danlos Syndrome / Reproducibility of Results / Noonan syndrome / Cardiomyopathies / Pericardium / Hypertrophic Cardiomyopathy / Aorta / Turner Syndrome / Gaucher Disease / Friedreich Ataxia / Myxoma / Heart Diseases

A composite polymer nanoparticle overcomes multidrug resistance and ameliorates doxorubicin-associated cardiomyopathy

Nanoparticles / Humans / Mice / Curcumin / Animals / Multiple Myeloma / Male / Glutathione / Doxorubicin / Cardiomyopathies / Multiple Myeloma / Male / Glutathione / Doxorubicin / Cardiomyopathies

Cardiac sarcoidosis

Magnetic Resonance Imaging / Sarcoidosis / Humans / Myocardium / Prognosis / Implantable defibrillators-cardioverters / Cardiomyopathies / Heart Transplantation / Implantable defibrillators-cardioverters / Cardiomyopathies / Heart Transplantation

Porous acellular bovine pericardia seeded with mesenchymal stem cells as a patch to repair a myocardial defect in a syngeneic rat model

Biomaterials / Tissue Engineering / Regeneration / Multidisciplinary / Porosity / Animals / Mesenchymal Stem Cell / Glycosaminoglycan / Cattle / Rats / Rat Model / Cardiomyopathies / Right Ventricle / Pericardium / Materials Testing / Cell free System / Biocompatible Materials / Mesenchymal Stromal Cells / Animals / Mesenchymal Stem Cell / Glycosaminoglycan / Cattle / Rats / Rat Model / Cardiomyopathies / Right Ventricle / Pericardium / Materials Testing / Cell free System / Biocompatible Materials / Mesenchymal Stromal Cells

Cardiac sarcoidosis

Magnetic Resonance Imaging / Sarcoidosis / Humans / Myocardium / Prognosis / Implantable defibrillators-cardioverters / Cardiomyopathies / Heart Transplantation / Implantable defibrillators-cardioverters / Cardiomyopathies / Heart Transplantation
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