Cystic Fibrosis

A novel natural product compound enhances cAMP-regulated chloride conductance of cells expressing CFTR[delta]F508

Molecular Medicine / Cystic Fibrosis / Drug Discovery / Cell line / Humans / cyclic AMP / Natural Product / Chloride Channel / Genistein / Biological Factors / Protein Binding / Electric Conductivity / Plasma Membrane / Chemical Structure / Biochemistry and cell biology / Dimerization / cyclic AMP / Natural Product / Chloride Channel / Genistein / Biological Factors / Protein Binding / Electric Conductivity / Plasma Membrane / Chemical Structure / Biochemistry and cell biology / Dimerization

Bactericidal properties of group IIa secreted phospholipaseA2againstPseudomonasaeruginosa clinical isolates

Cystic Fibrosis / Medical Microbiology / Phospholipids / Biological Sciences / Humans / Pseudomonas aeruginosa / Enzyme / Gram Positive Bacteria / Gram-negative bacteria / Epithelial cells / Time Dependent / Trachea / Pseudomonas Aeruginosa / Cell Wall / High-protein Diet / Hydrolysis / Cell Survival / Sodium Chloride / Pseudomonas aeruginosa / Enzyme / Gram Positive Bacteria / Gram-negative bacteria / Epithelial cells / Time Dependent / Trachea / Pseudomonas Aeruginosa / Cell Wall / High-protein Diet / Hydrolysis / Cell Survival / Sodium Chloride

Polymorphonuclear leucocytes consume oxygen in sputum from chronic Pseudomonas aeruginosa pneumonia in cystic fibrosis

Cystic Fibrosis / Humans / Reactive Oxygen Species / Chronic Disease / Female / Thorax / Male / Young Adult / Pseudomonas aeruginosa / NADPH oxidase / Clinical Sciences / Middle Aged / Neutrophils / Phagocytosis / Adult / Pseudomonas Aeruginosa / Sputum / Superoxide Anion / Oxygen Consumption / Superoxides / Respiratory Burst / Thorax / Male / Young Adult / Pseudomonas aeruginosa / NADPH oxidase / Clinical Sciences / Middle Aged / Neutrophils / Phagocytosis / Adult / Pseudomonas Aeruginosa / Sputum / Superoxide Anion / Oxygen Consumption / Superoxides / Respiratory Burst

Polymorphonuclear leucocytes consume oxygen in sputum from chronic Pseudomonas aeruginosa pneumonia in cystic fibrosis

Cystic Fibrosis / Humans / Reactive Oxygen Species / Chronic Disease / Female / Thorax / Male / Young Adult / Pseudomonas aeruginosa / NADPH oxidase / Clinical Sciences / Middle Aged / Neutrophils / Phagocytosis / Adult / Pseudomonas Aeruginosa / Sputum / Superoxide Anion / Oxygen Consumption / Superoxides / Respiratory Burst / Thorax / Male / Young Adult / Pseudomonas aeruginosa / NADPH oxidase / Clinical Sciences / Middle Aged / Neutrophils / Phagocytosis / Adult / Pseudomonas Aeruginosa / Sputum / Superoxide Anion / Oxygen Consumption / Superoxides / Respiratory Burst

Perception of disease severity in adult patients with cystic fibrosis* Percepção da gravidade da doença em pacientes adultos com fibrose cística

Cystic Fibrosis / Patient Compliance / Disease Severity / Health Status / Clinical Data / Cross sectional Study / Respiratory Function / Cross sectional Study / Respiratory Function

Percepção da gravidade da doença em pacientes adultos com fibrose cística* Perception of disease severity in adult patients with cystic fibrosis

Cystic Fibrosis / Patient Compliance / Disease Severity / Health Status / Clinical Data / Cross sectional Study / Respiratory Function / Cross sectional Study / Respiratory Function

Percepção da gravidade da doença em pacientes adultos com fibrose cística* Perception of disease severity in adult patients with cystic fibrosis

Cystic Fibrosis / Patient Compliance / Disease Severity / Health Status / Clinical Data / Cross sectional Study / Respiratory Function / Cross sectional Study / Respiratory Function

Perception of disease severity in adult patients with cystic fibrosis* Percepção da gravidade da doença em pacientes adultos com fibrose cística

Perception / Health Behavior / Cystic Fibrosis / Self Care / Prospective studies / Humans / Female / Male / Young Adult / Patient Compliance / Disease Severity / Health Status / Clinical Data / Cross sectional Study / Cross Sectional Studies / Respiratory Function / Humans / Female / Male / Young Adult / Patient Compliance / Disease Severity / Health Status / Clinical Data / Cross sectional Study / Cross Sectional Studies / Respiratory Function

Adesão ao tratamento em pacientes com fibrose cística

Cystic Fibrosis / Patient Compliance / Health Professionals / Enzyme / Clinical Data / Cross sectional Study

Percepção da gravidade da doença em pacientes adultos com fibrose cística

Cystic Fibrosis / Disease Severity / Health Status / Cross sectional Study / Respiratory Function

Padrões ventilatórios na espirometria em pacientes adolescentes e adultos com fibrose cística

Cystic Fibrosis / Lung Function / Functional impairment / Cross sectional Study / Respiratory Function / Control Group

Magnetic resonance of the lung: A step forward in the study of lung disease | Ressonância magnética de pulmão: Um novo passo no estudo das doenças pulmonares

Magnetic Resonance Imaging / Cystic Fibrosis / Pulmonary Hypertension / Humans / Pulmonary Embolism / Lung Diseases / Lymph nodes / Lung Diseases / Lymph nodes

Arquitetura do sono e perfil respiratório polissonográfico de crianças e adolescentes com fibrose cística

Cystic Fibrosis / Adolescent / Humans / Child / Polysomnography / Chronic obstructive pulmonary disease
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