Hepatic lymphangioma - a case report

Pediatr Surg Int (2000) 16: 515±516

Ó Springer-Verlag 2000

CASE REPORT

Chee-Chee Koh á Jin-Cherng Sheu

Hepatic lymphangioma ± a case report

Accepted: 31 June 1999

Abstract A patient presented with a huge, pedunculated abdominal cystic lymphangioma arising from the quadrate lobe of the liver near the round ligament. Microscopically, dilated hepatic ducts with scant liver tissue could be recognized in the main cyst. A review of the literature reveals no previous report of a lymphangioma arising in this manner or from this area. Key words Intra-abdominal lymphangioma á Hepatic lymphangioma

Introduction Lymphangioma of the liver is an extremely rare benign tumor that is usually observed in children and adolescents. In most reported cases there is di€use involvement of multiple organs including the liver, spleen, kidneys, skeleton, gastrointestinal (GI) tract, mesentery, lungs, and somatic soft tissue. We report an exceptional case of a multiloculated cystic lymphangioma in the liver and round ligament with no other organs involved.

C.-C. Koh (&) á J.-C. Sheu Department of Pediatric Surgery, Mackay Memorial Hospital, No. 92 Chung-Shan North Road Sec 2, Taipei, Taiwan 10449, Republic of China

Case report A 6-month-old, previously-well boy had a 2-month history of increasing abdominal girth. There were no signi®cant abnormalities on physical examination except for marked generalized distention of the abdomen. Results of laboratory studies, including a complete blood count, electrolytes, renal and liver function tests, and b-human chorionic gonadotropin were within normal limits except for an alkaline phosphatase level of 195 IU/l (25±100 IU/ l), lactate dehydrogenase 249 IU/l (90± 200 IU/l), and a-fetoprotein 16.72 ng/ml (