Cystic Fibrosis

A Novel Natural Product Compound Enhances cAMP-Regulated Chloride Conductance of Cells Expressing CFTR[delta]F508

Molecular Medicine / Cystic Fibrosis / Drug Discovery / Cell line / Humans / cyclic AMP / Natural Product / Chloride Channel / Genistein / Biological Factors / Protein Binding / Electric Conductivity / Plasma Membrane / Chemical Structure / Biochemistry and cell biology / Dimerization / cyclic AMP / Natural Product / Chloride Channel / Genistein / Biological Factors / Protein Binding / Electric Conductivity / Plasma Membrane / Chemical Structure / Biochemistry and cell biology / Dimerization

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A Novel Natural Product Compound Enhances cAMP-Regulated Chloride Conductance of Cells Expressing CFTRF508

Molecular Medicine / Cystic Fibrosis / Drug Discovery / Cell line / Humans / cyclic AMP / Natural Product / Chloride Channel / Genistein / Biological Factors / Protein Binding / Electric Conductivity / Plasma Membrane / Chemical Structure / Biochemistry and cell biology / Dimerization / cyclic AMP / Natural Product / Chloride Channel / Genistein / Biological Factors / Protein Binding / Electric Conductivity / Plasma Membrane / Chemical Structure / Biochemistry and cell biology / Dimerization

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Autosomal dominant polycystic kidney disease: possible influences of single nucleotide polymorphism in cytokine genes; Doença renal policística autossômica dominante: possíveis influências de polimorfismos de um único nucleotídeo em genes de citocinas

Genetics / Immunology / Cystic Fibrosis / Cytogenetic / Kidney diseases / Acute kidney injury / Chronic kidney disease / Cytokines / Single Nucleotide Polymorphisms (SNPs) / Proinflammatory Cytokines (TNF alpha and İnterleukin beta) / Proinflammatory Cytokines / Immunogenetics / Cytogenetics / SNP associated genomics / Acute renal failure / Kidney / Genetica / Renal failure / End stage renal diseases / SNPs review / Lead Immune Cytokine / Chronic Renal Failure / Cytokine / ADPKD / Snp / Imunologia / Cytokinesis / Antiinflammatory Cytokines / Polimorfismo De Base úNica / Polycystic kidney disease / Cytokines and receptors / Inflammatory Cytokines / DRP / SNP's / Autosomal Dominant Polycystic Kidney / Doença Renal Policística Autossômica Dominante / Doença Renal Policística Do Adulto / Doença Renal Policística Tipo 1 / Polycyclic Failure / DRPAD / Polimorfimos / Doença Do Rim Policístico / Imunogenética / Acute kidney injury / Chronic kidney disease / Cytokines / Single Nucleotide Polymorphisms (SNPs) / Proinflammatory Cytokines (TNF alpha and İnterleukin beta) / Proinflammatory Cytokines / Immunogenetics / Cytogenetics / SNP associated genomics / Acute renal failure / Kidney / Genetica / Renal failure / End stage renal diseases / SNPs review / Lead Immune Cytokine / Chronic Renal Failure / Cytokine / ADPKD / Snp / Imunologia / Cytokinesis / Antiinflammatory Cytokines / Polimorfismo De Base úNica / Polycystic kidney disease / Cytokines and receptors / Inflammatory Cytokines / DRP / SNP's / Autosomal Dominant Polycystic Kidney / Doença Renal Policística Autossômica Dominante / Doença Renal Policística Do Adulto / Doença Renal Policística Tipo 1 / Polycyclic Failure / DRPAD / Polimorfimos / Doença Do Rim Policístico / Imunogenética

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Polymorphonuclear leucocytes consume oxygen in sputum from chronic Pseudomonas aeruginosa pneumonia in cystic fibrosis

Cystic Fibrosis / Humans / Reactive Oxygen Species / Chronic Disease / Female / Thorax / Male / Young Adult / Pseudomonas aeruginosa / NADPH oxidase / Clinical Sciences / Middle Aged / Neutrophils / Phagocytosis / Adult / Pseudomonas Aeruginosa / Sputum / Superoxide Anion / Oxygen Consumption / Superoxides / Respiratory Burst / Thorax / Male / Young Adult / Pseudomonas aeruginosa / NADPH oxidase / Clinical Sciences / Middle Aged / Neutrophils / Phagocytosis / Adult / Pseudomonas Aeruginosa / Sputum / Superoxide Anion / Oxygen Consumption / Superoxides / Respiratory Burst

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Programa de triagem neonatal para fibrose cística no estado do Paraná: avaliação após 30 meses de sua implantação

Program Evaluation / Cystic Fibrosis / Brazil / Humans / Female / Male / Trypsin / Incidence / Newborn Infant / Biological markers / Sweat / Sodium Chloride / Male / Trypsin / Incidence / Newborn Infant / Biological markers / Sweat / Sodium Chloride

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Adesão ao tratamento em pacientes com fibrose cística

Perception / Nonparametric Statistics / Cystic Fibrosis / Diet / Exercise therapy / Prospective studies / Humans / Child / Female / Male / Patient Compliance / Health Professionals / Enzyme / Spirometry / Adult / Clinical Data / Cross sectional Study / Cross Sectional Studies / Health Personnel / Prospective studies / Humans / Child / Female / Male / Patient Compliance / Health Professionals / Enzyme / Spirometry / Adult / Clinical Data / Cross sectional Study / Cross Sectional Studies / Health Personnel

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A r t ig o O r ig in a l Fibrose cística em adultos: aspectos clínicos e espirométricos* Cystic fibrosis in adults clinical and spirometric aspects

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Noncirrhotic presinusoidal portal hypertension is common in cystic fibrosis associated liver disease

Cystic Fibrosis / Hepatology / Biopsy / Humans / Portal hypertension / Liver Cirrhosis / Liver / Clinical Sciences / Retrospective Studies / Portal vein / Liver Cirrhosis / Liver / Clinical Sciences / Retrospective Studies / Portal vein

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Flagellin of Pseudomonas aeruginosa inhibits Na+ transport in airway epithelia

Physiology / Cystic Fibrosis / Biology / Membrane Proteins / Cell Biology / Patch-clamp and imaging techniques / Response Inhibition / Humans / Nitriles / Mice / Animals / Flagella / Calcium Signaling / Medical Physiology / Mitogen Activated Protein Kinase / Pseudomonas aeruginosa / Gram-negative bacteria / Epithelial cells / Sodium / Trachea / Voltage-Gated Sodium Channels / Respiratory Tract Infections / Pseudomonas Aeruginosa / Ion Transport / Biochemistry and cell biology / Adenosine Triphosphate / Flagellin / ENaC / Patch-clamp and imaging techniques / Response Inhibition / Humans / Nitriles / Mice / Animals / Flagella / Calcium Signaling / Medical Physiology / Mitogen Activated Protein Kinase / Pseudomonas aeruginosa / Gram-negative bacteria / Epithelial cells / Sodium / Trachea / Voltage-Gated Sodium Channels / Respiratory Tract Infections / Pseudomonas Aeruginosa / Ion Transport / Biochemistry and cell biology / Adenosine Triphosphate / Flagellin / ENaC

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Adaptação cultural e propriedades psicométricas iniciais do instrumento DISABKIDS ® – Cystic Fibrosis Module – versão brasileira

Psychometrics / Cystic Fibrosis / Quality of life / Brazil / Adolescent / Humans / Child / Female / Male / Questionnaires / Cross Sectional Studies / Humans / Child / Female / Male / Questionnaires / Cross Sectional Studies

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Diagnóstico de ABPA em pacientes portadores de fibrose cística: utilidade clínica da pesquisa de IgE específica contra alérgenos recombinantes do Aspergillus fumigatus

Cystic Fibrosis / Adolescent / Allergic bronchopulmonary aspergillosis / Humans / Child / Confidence intervals / Allergens / Immunoglobulin E / Aspergillus fumigatus / Adult / Cross Sectional Studies / Confidence intervals / Allergens / Immunoglobulin E / Aspergillus fumigatus / Adult / Cross Sectional Studies

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[Gas exchanges. Mucoviscidosis]

Carbon Dioxide / Cystic Fibrosis / Humans / Anoxia / Circadian Rhythm / Oxygen / Oximetry / Blood gas analysis / Pulmonary Gas Exchange / Oxygen / Oximetry / Blood gas analysis / Pulmonary Gas Exchange

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Human cystic fibrosis embryonic stem cell lines derived on placental mesenchymal stromal cells

Genetics / Tissue Engineering / Cystic Fibrosis / Induced Pluripotent Stem Cells (I Psc) / Human embryonic stem cell / Stem Cell / Cell line / Cell Differentiation / Humans / Genetic Testing / Mutation / Placenta / Female / Embryonic Stem Cell / Plant tissue Culture Techniques / Polymerase Chain Reaction / Drug Screening / Karyotyping / Embryonic Stem Cells / Stromal Cells / Mesenchymal Stromal Cells / Gene expression profiling / Stem Cell / Cell line / Cell Differentiation / Humans / Genetic Testing / Mutation / Placenta / Female / Embryonic Stem Cell / Plant tissue Culture Techniques / Polymerase Chain Reaction / Drug Screening / Karyotyping / Embryonic Stem Cells / Stromal Cells / Mesenchymal Stromal Cells / Gene expression profiling

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Tracheal distensibility in cystic fibrosis

Cystic Fibrosis

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Noncirrhotic presinusoidal portal hypertension is common in cystic fibrosis-associated liver disease

Cystic Fibrosis / Hepatology / Biopsy / Humans / Portal hypertension / Liver Cirrhosis / Liver / Clinical Sciences / Retrospective Studies / Portal vein / Liver Cirrhosis / Liver / Clinical Sciences / Retrospective Studies / Portal vein

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A Novel Natural Product Compound Enhances cAMP-Regulated Chloride Conductance of Cells Expressing CFTRF508

Cystic Fibrosis / Drug Discovery / Cell line / Humans / cyclic AMP / Natural Product / Chloride Channel / Genistein / Biological Factors / Protein Binding / Electric Conductivity / Plasma Membrane / Chemical Structure / Biochemistry and cell biology / Dimerization / Natural Product / Chloride Channel / Genistein / Biological Factors / Protein Binding / Electric Conductivity / Plasma Membrane / Chemical Structure / Biochemistry and cell biology / Dimerization

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